Vertebral solitary bone plasmacytoma in a young adult with Trisomy 21: A case report.
Autor: Bouattour, Nadia; Hdiji, Olfa; Hachicha, Anis; Kammoun, Brahim; Sakka, Salma; Farhat, Nouha; Hajkacem, Hanen; Kolsi, Fatma; Charfi, Slim; Dammak, Mariem; Boudawara, Zaher; Boudawara, Tahya; Mhiri, Chokri
Publication year: 2020
The journal of spinal cord medicine
issn:2045-7723 1079-0268
doi: 10.1080/10790268.2018.1557866
Abstract:
Context: Solitary bone plasmacytoma (SBP) are rare lesions, accounting for less than 5% of all plasma cell proliferations. We describe a case of a 21-year-old female with Trisomy 21 presenting with cauda equina compression from an SBP. Findings: Solitary bone plasmacytoma (SBP) is a rare primary bone tumor. It is characterized by monoclonal proliferation of malignant plasma cells localized to a bone segment, without signs of systemic invasion. The vertebral location is the most common. It preferentially affects men during their 5th or 6th decade. Clinical relevance: We report the first association between solitary bone plasmacytoma and Trisomy 21.
Language: eng
Rights:
Pmid: 30557097
Tags: Humans; Female; Male; Adult; Young Adult; *Spinal Cord Injuries; *Bone Neoplasms; *Down Syndrome/complications; *Plasmacytoma/complications/diagnosis; Cauda equina syndrome; Extramedullary plasmacytoma; Plasmacytoma; Solitary bone plasmacytoma; Trisomy 21
Link: https://pubmed.ncbi.nlm.nih.gov/30557097/