Annuloplasty for Aortic Regurgitation in Infantile Takayasu Arteritis: A Case Report.
Autor: Linnemeier, Laura; Sharma, Richa; Srivastava, Nayan; Turrentine, Mark
Publication year: 2020
World journal for pediatric & congenital heart surgery
issn:2150-136X 2150-1351
doi: 10.1177/2150135117692979
Abstract:
Aortic regurgitation (AR) is a life-threatening complication of Takayasu arteritis (TA). Takayasu arteritis is a large-vessel vasculitis with a predominance in young adolescent and adult females. Inflammation involves the aorta and its major branches resulting in arterial dilatation, stenosis, aneurysm, occlusion, and thrombosis formation. Pediatric TA cases have been reported to also cause severe complications such as coronary aneurysms, retinopathy, and hypertension due to renovascular stenosis. In this report, we present a rare occurrence of infantile TA with severe AR requiring surgical intervention after failing medical therapy. Due to the patient’s age and clinical status, a valve-sparing aortic annuloplasty with aortoplasty was performed.
Language: eng
Rights:
Pmid: 28673107
Tags: Humans; Male; inflammation; Infant; Computed Tomography Angiography; echocardiography; Echocardiography, Transesophageal; aortic valve annuloplasty; Aortic Valve Insufficiency/diagnosis/etiology/*surgery; Aortic Valve/diagnostic imaging/*surgery; Balloon Valvuloplasty/*methods; infant; Takayasu Arteritis/*complications/diagnosis
Link: https://pubmed.ncbi.nlm.nih.gov/28673107/