Acquired von Willebrand Syndrome in an Infant With Coarctation of the Aorta and Williams Syndrome.
Autor: Cochran, Clinton D.; Madani, Rohit S.; Peltier, Daniel; Pipe, Steven; Owens, Sonal T.
Publication year: 2020
World journal for pediatric & congenital heart surgery
issn:2150-136X 2150-1351
doi: 10.1177/2150135117733942
Abstract:
An infant with coarctation of the aorta and Williams syndrome was noted to have petechiae in cardiology clinic prior to planned surgical intervention. Workup revealed acquired von Willebrand syndrome secondary to the high shear force generated by the aortic coarctation. He was treated with intra- and postoperative Humate P; there were no postoperative bleeding complications. His acquired von Willebrand syndrome resolved postoperatively.
Language: eng
Rights:
Pmid: 29113538
Tags: Humans; Male; Infant, Newborn; Echocardiography; congenital heart disease; *Abnormalities, Multiple; Vascular Surgical Procedures/methods; acquired von Willebrand syndrome; Aortic Coarctation/blood/*diagnosis/surgery; blood; coagulation/anticoagulation; coarctation of the aorta; von Willebrand Diseases/*diagnosis/surgery; von Willebrand Factor/*metabolism; Williams syndrome; Williams Syndrome/blood/*diagnosis/surgery
Link: https://pubmed.ncbi.nlm.nih.gov/29113538/
